Popcorn-scentedurine typically occurs as a result of dietary factors or dehydration and is no cause for concern. One of the most common culprits behind sweet-scentedurine is diabetes mellitus. When diabetes is uncontrolled, excess glucose can spill into the urine, resulting in a sweet fragrance. A mother has opened up about her daughter's rare genetic condition that causes her to smell sweet like syrup and have maple-scentedurine. Why is H's urinesweet smelling like maple syrup? I kept smelling syrup tonight while changing H to get her ready for bed. She usually wears the same… The most noticeable symptom of the condition is sweetscentedurine that may smell similar to maple syrup. The disease prevents the body from breaking down amino acids effectively. While variations in urine smell are common and often harmless, a persistent or unusual odor, particularly one described as resembling ants or having a sweetscent... Urine can reflect hydration, dietary habits, or even signs of medical conditions. Below, we break down what different urine signs may mean and how they relate to your health. If your urine has a fruity or sweet smell, it could be a sign of high blood sugar, as your body releases excess glucose through your urine. A popcorn smell or sweet-smelling urine is often an early indicator of untreated or undiagnosed diabetes. Diabetes affects your blood sugar levels and causes high ketone levels. The most obvious symptom of MSUD is the sweet-scentedurine. If left untreated, MSUD can lead to seizures, comas, and even death.